{"id":3102,"date":"2023-12-15T16:54:47","date_gmt":"2023-12-15T08:54:47","guid":{"rendered":"https:\/\/twcr.tw\/?p=3102"},"modified":"2024-01-24T16:30:20","modified_gmt":"2024-01-24T08:30:20","slug":"%e7%99%8c%e7%99%bb%e7%ac%ac112005%e8%99%9f%e9%80%9a%e7%9f%a5%e6%96%87-%e5%9b%a0%e6%87%89%e7%99%8c%e7%97%87%e7%99%bb%e8%a8%98%e5%af%a6%e5%8b%99%e4%bd%9c%e6%a5%ad%e4%b9%8b%e9%9c%80%e6%b1%82%ef%bc%8c","status":"publish","type":"post","link":"https:\/\/twcr.tw\/?p=3102","title":{"rendered":"[\u764c\u767b\u7b2c112005\u865f\u901a\u77e5\u6587] 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(\u542b)\u5e74\u524d\u8a3a\u65b7\u4e4b\u500b\u6848\uff0c\u8acb\u52d9\u5fc5\u65bc113\u5e742\u670829\u65e5\u524d\u5b8c\u6210\u764c\u75c7\u500b\u6848\u4e94\u5e74\u8ffd\u8e64\u8cc7\u6599\u7533\u5831\uff0c\u4ee5\u514d\u5f71\u97ff\u7576\u5e74\u5ea6\u4e4b\u7d93\u8cbb\u6838\u92b7\u8a08\u7b97\u8207113\u5e74\u8ffd\u8e64\u7387\u6210\u7e3e\u3002<\/p>\n<p>\u56db\u3001\u81ea113\u5e74\u7b2c\u4e00\u5b63\u8d77\uff0c\u6240\u6709\u7533\u5831\u4e4b\u764c\u75c7\u500b\u6848\u5747\u5168\u9762\u63a1\u7528112\u5e7412\u6708\u4fee\u8a02\u4e4b107\u5e74v.6\u300c\u53f0\u7063\u764c\u75c7\u767b\u8a18\u9577\u8868\/\u77ed\u8868\u6458\u9304\u624b\u518a\u300d\u3001\u300c\u764c\u75c7\u90e8\u4f4d\u7279\u5b9a\u56e0\u5b50\u7de8\u78bc\u624b\u518a\u300d\u898f\u5247\u7533\u5831\u3002\u6709\u95dc107\u5e74\u7248\u53f0\u7063\u764c\u75c7\u767b\u8a18\u6458\u9304\u624b\u518a-112\u5e74\u4fee\u8a02\u7248\uff0c\u8acb\u81f3\u53f0\u7063\u764c\u75c7\u767b\u8a18\u4e2d\u5fc3\u7db2\u7ad9<a href=\"https:\/\/twcr.tw\/?page_id=1809\">https:\/\/twcr.tw\/?page_id=1809<\/a>\u4e0b\u8f09\u3002<\/p>\n<p>\u4e94\u3001107\u5e74\u7248\u53f0\u7063\u764c\u75c7\u767b\u8a18\u6458\u9304\u624b\u518a-112\u5e74\u4fee\u8a02\u7248\uff0c\u4e3b\u8981\u4fee\u6539\u5167\u5bb9\u5982\u4e0b\uff1a<\/p>\n<p>(1) \u70ba\u80fd\u5340\u5206\u95cc\u5c3e\u7d44\u7e54\u578b\u614b(M-code 8480)\u70baLow grade appendiceal mucinous neoplasm (LAMN)\u6216High grade appendiceal mucinous neoplasm (HAMN)\uff0c\u300c\u81e8\u5e8a\u5206\u7d1a\/\u5206\u5316\u300d\u8207\u300c\u75c5\u7406\u5206\u7d1a\/\u5206\u5316\u300d\u6b04\u4f4d\u65b0\u589e\u7de8\u78bcL\u548cH\u3002<\/p>\n<p>(2) \u300c\u81e8\u5e8aT\u300d\u8207\u300c\u75c5\u7406T\u300d\u6b04\u4f4d\u65b0\u589e\u7de8\u78bcISLA\uff0c\u5b9a\u7fa9\u70baTis(LAMN)\u3002<\/p>\n<p>(3) 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(Lu-177)\uff0c\u6b64\u70ba\u4e00\u7a2e\u80dc\u80bd\u53d7\u9ad4\u653e\u5c04\u6838\u7a2e\u6cbb\u7642Peptide receptor radionuclide therapy (PRRT)\u3002<\/p>\n<p>(6) \u300c\u9996\u6b21\u5fa9\u767c\u6216\u764c\u75c7\u72c0\u614b\u8ffd\u8e64\u65e5\u671f\u300d\u6b04\u4f4d\u4fee\u6539\u7de8\u78bc\u6307\u5f15\u5b9a\u7fa9\uff0c\u5176\u8ffd\u8e64\u65e5\u671f\u53ef\u4ee5\u63a1\u7528\u500b\u6848\u81f3\u91ab\u9662\u5c31\u8a3a\u65e5\u671f\uff0c\u6b64\u5c31\u8a3a\u65e5\u671f\u4e0d\u9650\u65bc\u764c\u75c7\u9580\u8a3a\u3002<\/p>\n<p>(7) \u80f0\u81df\u764cSSF4\u8207\u4e73\u764cSSF10\u300cKi-67\u300d\u6b04\u4f4d\u65b0\u589e\u7de8\u78bc\u6307\u5f15\u5b9a\u7fa9\uff0c\u82e5\u6aa2\u9a57\u503c\u5c0f\u65bc1%\u4ee5\u4e0b\u7684\u500b\u6848\uff0c\u65b0\u589e\u7de8\u78bc\u5b9a\u7fa9A01-A09\u3002\u4f8b\u5982\uff1a\u75c5\u7406\u5831\u544a\u8a18\u8f09Ki-67\u70ba0.3%\uff0c\u7de8\u78bc\u70baA03\u3002<\/p>\n<p>(8) \u4e73\u764cSSF7\u300cHER2\u514d\u75ab\u7d44\u7e54\u5316\u5b78\u6cd5\u7684\u5be6\u9a57\u6578\u503c\u300d\u6b04\u4f4d\uff0c\u56e0\u8fd1\u5e74Low HER2\u8cc7\u8a0a\u6f38\u53d7\u91cd\u8996\uff0c\u7576ISH\u6aa2\u6e2c\u7d50\u679c\u70ba\u9670\u6027\uff0c\u4e14IHC\u70ba1+\u62162+\u6642\uff0c\u4ecd\u9700\u8a18\u8f09IHC\u4e4b\u6aa2\u6e2c\u7d50\u679c\u3002\u6545\u65b0\u589e\u7de8\u78bc\u6307\u5f15\u53ca\u7de8\u78bc\u7bc4\u570d510-512\u3001520-522\u3001590-592\u3002<\/p>\n<p>(9) \u4e73\u764c\u3001\u5b50\u5bae\u9ad4\u764c\u4e4bSSF1\u300c\u52d5\u60c5\u6fc0\u7d20\u63a5\u53d7\u9ad4\u6aa2\u6e2c(ERA) \u300d\u8207SSF2\u300c\u9ec3\u9ad4\u6fc0\u7d20\u63a5\u53d7\u9ad4\u6aa2\u6e2c(PRA)\u300d\u6b04\u4f4d\u4fee\u6539\u7de8\u78bc\u6307\u5f15\u539f\u5247\uff0c\u7576\u55ae\u9846\u816b\u7624\u55ae\u4e00\u539f\u767c\u4e4b\u500b\u6848\u61c9\u512a\u5148\u6458\u9304\u624b\u8853\u5207\u9664\u539f\u767c\u90e8\u4f4d\u6700\u5927\u816b\u7624\u9ad4\u7a4d\u7684\u75c5\u7406\u5831\u544a\u6578\u503c\uff1b\u82e5\u70ba\u591a\u9846\u816b\u7624\u5206\u5225\u7686\u6709\u967d\u6027\u767e\u5206\u6bd4\u6aa2\u9a57\u503c\uff0c\u5247\u512a\u5148\u6458\u9304\u53cd\u61c9\u6bd4\u4f8b\u8f03\u9ad8\u4e4b\u6aa2\u9a57\u503c\u3002<\/p>\n<p>(10)\u767d\u8840\u75c5SSF1\u300c\u767d\u8840\u75c5\u67d3\u8272\u9ad4\u6aa2\u67e5\u7684\u8a55\u4f30\u300d\u4fee\u6539\u7de8\u78bc004\u4e4b\u5b9a\u7fa9\uff0c\u65b0\u589e\u300ct(9;11)(p22;q23)\u300d\u3002<\/p>\n<p>\u516d\u3001\u6700\u65b0AJCC Version 9\u65bc2023\u5e74\u51fa\u7248\u5916\u9670\u764c\u3001\u795e\u7d93\u5167\u5206\u6ccc\u816b\u7624(\u5305\u542b\u80c3\u3001\u5341\u4e8c\u6307\u8178\u8207\u6cd5\u7279\u58fa\u8179\u3001\u7a7a\u8178\u8207\u8ff4\u8178\u3001\u95cc\u5c3e\u3001\u7d50\u76f4\u8178\u3001\u80f0\u7b49\u90e8\u4f4d)\u4e4b\u764c\u75c7\u5206\u671f\u7cfb\u7d71\uff0c\u9069\u7528\u65bc2024\u5e741\u67081\u65e5\u8d77\u65b0\u8a3a\u65b7\u4e4b\u500b\u6848\uff0c\u76f8\u95dcTNM\u8207Stage\u7de8\u78bc\u5c0d\u61c9\u8868\uff0c\u8207\u6bd4\u5c0d\u524d\u5f8c\u7248\u672c\u5dee\u7570\u8655\uff0c\u8acb\u53c3\u8003\u9644\u4ef6\u4e00\u3002<\/p>\n<p>\u4e03\u3001\u81ea2024\u5e741\u67081\u65e5\u8d77\u65b0\u8a3a\u65b7\u70ba\u5b50\u5bae\u9ad4\u764c\u500b\u6848\uff0cFIGO\u671f\u5225\u70ba\u5fc5\u586b\u6b04\u4f4d\uff1b\u6700\u65b0FIGO 2023\u5e74\u65b0\u7248\u9069\u7528\u65bc2024\u5e741\u67081\u65e5\u8d77\u65b0\u8a3a\u65b7\u4e4b\u5b50\u5bae\u5167\u819c\u764c\u500b\u6848\uff0c\u5728\u300c\u5176\u4ed6\u5206\u671f\u7cfb\u7d71\u671f\u5225(\u75c5\u7406)\u300d\u6b04\u4f4d\uff0c\u8acb\u4f9dFIGO 2023\u5e74\u7248\u7533\u5831(\u9644\u4ef6\u4e8c)\uff0c\u82e5\u5b50\u5bae\u9ad4\u764c\u7d44\u7e54\u5f62\u614b\u975e\u70ba\u5b50\u5bae\u5167\u819c\u764c\u8005\uff0c\u61c9\u4f9d\u539fFIGO 2009\u5e74\u7248\u7533\u5831\u3002<\/p>\n<p>\u524d\u8ff0\u516d\u3001\u4e03\u9ede\uff0c\u570b\u6c11\u5065\u5eb7\u7f72\u5c07\u65bc12\u6708\u5e95\u524d\u767c\u6587\u901a\u77e5\u5404\u91ab\u9662\uff0c\u8acb\u591a\u52a0\u7559\u610f\u3002<\/p>\n<p>\u516b\u3001\u4f9d\u64da2023\u5e74\u51fa\u7248WHO Classification of Tumours\u7b2c5\u7248Paediatric Tumor\uff0c\u7d71\u6574\u6700\u65b0\u75c5\u7406\u7d44\u7e54\u578b\u614b\u4ee3\u78bc\u7533\u5831\u539f\u5247(\u9644\u4ef6\u4e09)\uff0c\u4e14\u9069\u7528\u65bc2023\u8a3a\u65b7\u5e74\u8d77\u500b\u6848\uff0c\u76f8\u95dc\u91cd\u9ede\u6458\u9304\u5982\u4e0b\uff1a<\/p>\n<p>(1) \u4f4d\u65bcTestis (C62._) \u7684Well differentiated neuroendocrine tumor (monodermal teratoma)\uff0c<strong>\u61c9\u7de8\u78bc\u70ba<\/strong><strong>9084\/3<\/strong>\u3002<\/p>\n<p>(2) \u4f4d\u65bc\u9aa8\u3001\u8edf\u9aa8\u3001\u95dc\u7bc0\u3001\u6216\u8edf\u7d44\u7e54(C40._, C41._, C47._, C49._)\u7684Round cell sarcoma with EWSR1-non-ETS fusions, Round cell sarcoma with EWSR1\/FUS::NFATC2, Round cell sarcoma with EWSR1::PATZ1\uff0c<strong>\u65b0\u589e\u7de8\u78bc\u70ba<\/strong><strong>9366\/3<\/strong>\u3002<\/p>\n<p>(3)<span style=\"color: #ff0000;\"><strong> [<\/strong><strong>\u66f4\u6b63\u6027\u614b\u78bc<\/strong><strong>]<\/strong><\/span>\u4e0b\u8ff03\u9805soft tissue (C47._,C49._)\uff1aPlaque-like dermatofibrosarcoma protuberans, Myxoid dermatofibrosarcoma protuberans, \u8207Dermatofibrosarcoma protuberans with myoid differentiation\uff0c\u7de8\u78bc\u66f4\u6b63\u70ba8832<span style=\"color: #ff0000;\">\/<strong>1<\/strong>\uff0c<strong>\u7121\u9700\u7533\u5831<\/strong><\/span>\u3002<\/p>\n<p>\u4e5d\u3001\u8fd1\u5e74\u4f9d\u64daWHO Classification of Tumours \u7b2c 5 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